un caso indimenticabile - sipps...amir mannarmn 1 alnn Ž01Ž nato 'inl nn nam. arngn pts ptl...
TRANSCRIPT
![Page 1: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/1.jpg)
Un Caso indimenticabile
Berardo Sarubbi, Giangiacomo Di NardoUnità Dipartimentale “Cardiopatie Congenite dell’Adulto (GUCH Unit)”
A.O.R.N Monaldi
Berardo Sarubbi, Giangiacomo Di NardoUnità Dipartimentale “Cardiopatie Congenite dell’Adulto (GUCH Unit)”
A.O.R.N Monaldi
![Page 2: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/2.jpg)
C.P. nato il 30.11.00•Taglio cesareo alla 35^ settimana perriscontro ECO fetale di Aritmia di ndd
•Peso alla nascita Kg. 3.200
•Buone condizioni emodinamiche
•Non anomalie cardiache associate
![Page 3: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/3.jpg)
![Page 4: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/4.jpg)
![Page 5: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/5.jpg)
![Page 6: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/6.jpg)
Caso Clinico
Sindrome del QT lungo Congenito
•Impossibilità ad applicare AICD
•Terapia con Mexiletina
•Terapia con Beta-bloccanti (??)
![Page 7: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/7.jpg)
![Page 8: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/8.jpg)
Caso Clinico
Sindrome del QT lungo Congenito
•Mexiletina per os 5mg/kg
•Propranololo per os 6mg/Kg
•Magnesio solfato
![Page 9: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/9.jpg)
![Page 10: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/10.jpg)
Int. J. Cardiol. 2011
![Page 11: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/11.jpg)
![Page 12: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/12.jpg)
![Page 13: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/13.jpg)
Pts with LQTS who experience ACA during the first year oflife are at very high risk for subsequent ACA or deathduring their next 10 yrs of life, and b-block might not beeffective in preventing fatal or near fatal cardiac events inthis high-risk subset JACC 2009
![Page 14: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/14.jpg)
Volume: 69.9 ccPeso: 145 gSpessore: 15.7 mmEnergia: 80 JLongevità: 5.4 anni
![Page 15: Un Caso indimenticabile - SIPPS...amir mannarmn 1 alnn Ž01Ž Nato 'Inl Nn Nam. arngn Pts Ptl Pt2 Pt3 Pt4 Pt5 Pt6 Pt7 Sex M F M M M Age at presentation 1 day 1 day 10 days 1 day 1](https://reader035.vdocumenti.com/reader035/viewer/2022071413/610bcd18c276442b29195b33/html5/thumbnails/15.jpg)
Paolo C. 14 anni, 38kg